Diethylcarbamazine (DEC)

LeAnne M. Fox, Amy D. Klion

Description

N,N-Diethyl-4-methylpiperazine-1-carboxamide dihydrogen citrate.

Available Products

1. DEC tablets (available from US Centers for Disease Control and Prevention): 50 mg.

2. DEC tablets can be found under other names in other countries, including Hetrazan®, Banocide® and Notézine®.

Indications

1. Treatment of Loa loa.

2. Prophylaxis for L. loa.

3. Treatment of lymphatic filariasis (Wuchereria bancrofti, Brugia malayi, Brugia timori).

4. Treatment of tropical pulmonary eosinophilia (TPE).

5. Treatment of Mansonella streptocerca infection (streptocerciasis).

Mode of Action

The mechanism of action of DEC is poorly understood. It has no filaricidal effect in vitro, but appears to render microfilariae more susceptible to destruction by host defense mechanisms through effects on the surface membrane [1] and parasite motility [2]. The mechanism of action against adult worms is unknown [1], although some studies have suggested that DEC compromises intracellular processing and transport of certain macromolecules to the plasma membrane [3].

Pharmacokinetics

Peak serum levels are achieved in 1–2 hours after a single oral dose and plasma half-life varies from 2–10 hours, depending on the urinary pH. DEC is excreted by both urinary and extra-urinary routes; more than 50% of the oral dose appears in acidic urine as the unchanged drug. Alkalinizing the urine can elevate plasma levels, prolong half-life and increase the therapeutic effect and toxicity of DEC.

Dose Adjustments in Renal Failure

Consider dose adjustment in severe renal impairment [4].

Dose Adjustments in Liver Failure

None.

Dose

Treatment of L. loa:

Adults and children >18 months of age: 3 mg/kg three times daily for 21 days.

Prophylaxis against L. loa:

Adults and children >18 months of age: 6 mg/kg up to 300 mg dose once weekly.

Treatment of lymphatic filariasis*:

Adults and children >18 months of age: 6 mg/kg/day divided in 3 doses for 12 consecutive days OR 6 mg/kg/day as a single dose.

Treatment of TPE:

Adults and children >18 months of age: 6 mg/kg/day divided in 3 doses for 14–21 days.

Route of Administration

Oral.

How to Give the Drug

Administering with food can lessen intestinal upset.

Adverse Events and Serious Adverse Events

Due to the Drug Itself

Gastrointestinal: nausea, gastrointestinal upset.

Systemic: drowsiness.

Other (rarely reported): rash.

Due to the Effect on the Parasite

Hematologic: eosinophilia.

Renal: hematuria, proteinuria.

Gastrointestinal: abdominal pain, nausea.

Neurologic (L. loa): headache and, rarely, neuropsychiatric problems, entrapment neuropathy or encephalopathy.

Skin and soft tissue: rash, subcutaneous nodules, angioedema, urticaria.

Lymphatic (W. bancrofti and Brugia spp): adenitis, lymphangitis and, rarely, acute lymphedema or hydrocele, scrotal nodules, epididymitis.

Systemic: fever, headache, malaise, myalgia, arthralgia, orthostatic hypotension.

Key Drug Interactions

None.

Contraindications

Onchocerciasis should be excluded in all patients with a consistent exposure history owing to the possibility of severe exacerbations of skin and eye involvement (Mazzotti reaction). DEC should be used with extreme caution in patients with circulating L. loa microfilarial levels >2500/mm3 owing to the potential for life-threatening side effects, including encephalopathy and renal failure. Neither steroids pretreatment nor slow dose escalation prevents these complications.

Use in Special Populations

Pregnancy

Category C.

Lactation

There is no information on DEC and breastfeeding.

Pediatrics

Safe and effective in children at least 18 months of age.

Elderly (Age > 60)

No adjustment.

Resistance

Not reported to date.

Storage

Room temperature, protected from light.

Availability in the USA

DEC is not currently licensed for commercial use in the USA, but is available to US-licensed physicians from the CDC under an Investigational New Drug (IND) protocol for treatment of loiasis and lymphatic filariasis and chemoprophylaxis of loiasis.

Comments on Use

Dosing recommendations are empiric as no formal studies have been conducted. Consequently, lower doses may be prudent depending on the initial microfilarial load, patient age, weight and/or medical status (e.g. renal disease).

References

1 Hawking F. Diethylcarbamazine and new compounds for the treatment of filariasis. Adv Pharmacol Chemother. 1979;16:129–194.

2 Langham ME, Kramer TR. The “in vitro” effect of diethylcarbamazine on the motility and survival of Onchocerca volvulus microfilariae. Tropenmed Parasitol. 1980;31:59–66.

3 Spiro RC, Parsons WG, Pery SK, et al. Inhibition of post-translational modification and surface expression of a melanoma-associated chondroitin sulfate proteoglycan by diethylcarbamazine or ammonium chloride. J Biol Chem. 1986;261:1521–1529.

4 Adjepon-Yamoah KK, Edwards G, Breckenridge AM, et al. The effect of renal disease on the pharmacokinetics of diethylcarbamazine in man. Br J Clin Pharm. 1982;13:829–834.

* For patients with microfilariae in the blood, some experts recommend starting with a lower dosage and scaling up: day 1: 50 mg, day 2: 50 mg three times/day, day 3: 100 mg three times/day, day 4–12: 6 mg/kg divided in three doses.